Pseudomyxoma retroperitonei is similar to pseudomyxoma peritonei except that the mucinous fluid accumulates in the retroperitoneum. It is very rare.
Synonym: extraperitoneal pseudomyxoma
In most cases the cause is rupture of a retrocecal appendiceal cystadenoma. Rare cases may be associated with colon or ovarian cancers.
Clinical features:
(1) palpable abdominal mass
(2) abdominal, back or lumbar pain
(3) fever
Laboratory findings:
(1) elevated serum CEA
(2) elevated CA19-9
(3) aspiration of mucoid fluid from the retroperitoneum
The location of the pseudomyxoma can be determined on MRI.
Complications:
(1) cutaneous fistula
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Specialty: Hematology Oncology, Surgery, general, Gastroenterology
ICD-10: ,
