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Description

Grotz et al reported criteria for diagnosing the Hypocomplementemic Urticarial Vasculitis Syndrome (HUVS). These are based on the criteria of Schwartz et al. The authors are from the Alfried Krupp Krankenhaus, Universitatsklinkum Essen, Medizinische Hochschule Hannover and St. Franziskus Hospital Munster.


 

Major criteria:

(1) chronic urticarial exanthem

(2) hypocomplementemia

 

Minor criteria:

(1) leukocytoclastic vasculitis

(2) arthralgia and/or arthritis

(3) episcleritis, conjunctivitis, and/or uveitis

(4) glomerulonephritis

(5) abdominal pain

(6) antibodies to C1q

 


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