Maron et al listed recommendations for physical activity and sports participation for patients with a genetic cardiovascular disease. The authors are from American Heart Association Committee on Exercise, Cardiac Rehabilitation and Prevention.
Genetic disorders considered:
(1) hypertrophic cardiomyopathy (HM)
(2) long QT syndrome (LQT)
(3) Marfan's syndrome (MS)
(4) arrhythmogenic right ventricular cardiomyopathy (ARVC)
(5) Brugada syndrome (BS)
METs |
Intensity of Exercise |
---|---|
> 6 |
high |
4 to 6 |
moderate |
< 4 |
low |
Recommendation |
Scale |
Code |
---|---|---|
strongly discouraged |
0 |
A |
generally not advised |
1 |
B |
intermediate (requires an individual risk assessment) |
2 or 3 |
C |
probably permitted |
4 |
D |
permitted |
5 |
E |
Factors that may impact recommendations for participation:
(1) risk for drowning
(2) risk from barotrauma
(3) risk from trauma secondary to transient loss of consciousness
High Intensity |
HM |
LQT |
MS |
ARVC |
BS |
---|---|---|---|---|---|
basketball |
A |
A |
C |
B |
C |
body building |
B |
B |
A |
B |
B |
ice hockey |
A |
A |
B |
A |
A |
racquetball or squash |
A |
C |
C |
A |
C |
rock climbing |
B |
B |
B |
B |
B |
running |
A |
A |
C |
A |
C |
skiing downhill |
C |
C |
C |
B |
B |
skiing cross country |
C |
C |
C |
B |
D |
soccer |
A |
A |
C |
A |
C |
tennis, singles |
A |
A |
C |
A |
C |
football, touch |
B |
B |
C |
B |
C |
windsurfing |
B |
A |
B |
B |
B |
Moderate Intensity |
HM |
LQT |
MS |
ARVC |
BS |
---|---|---|---|---|---|
baseball or softball |
C |
C |
C |
C |
D |
biking |
D |
D |
C |
C |
E |
hiking, modest |
D |
E |
E |
C |
D |
motorcycle riding |
C |
B |
C |
C |
C |
jogging |
C |
C |
C |
C |
E |
sailing |
C |
C |
C |
C |
D |
surfing |
C |
A |
B |
B |
B |
swimming , laps |
E |
A |
C |
C |
D |
tennis, doubles |
D |
D |
D |
C |
D |
treadmill |
E |
D |
D |
C |
E |
stationary bicycle |
E |
E |
D |
C |
E |
weightlifting, free weights |
B |
B |
A |
B |
A |
hiking |
C |
C |
C |
C |
D |
Low Intensity |
HM |
LQT |
MS |
ARVC |
BS |
---|---|---|---|---|---|
bowling |
E |
E |
E |
D |
E |
golf |
E |
E |
E |
D |
E |
horseback riding |
C |
C |
C |
C |
C |
scuba diving |
A |
A |
A |
A |
A |
skating (not team hockey) |
E |
E |
E |
D |
E |
snorkeling |
E |
A |
E |
D |
D |
weightlifting, non-free |
D |
D |
A |
D |
D |
walking, brisk |
E |
E |
E |
E |
E |
Specialty: Surgery, orthopedic, Hematology Oncology, Genetics
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