Parameters:
(1) DLCO as percent of predicted
(2) FVC as percent of predicted
(3) bibasilar rales
(4) radiographic evidence of fibrosis
(5) pulmonary hypertension
(6) oxygen required
Severity Grades: 0 (none) to 4 (endstage)
Criteria for Grade 0 (none) - all of the following:
(1) DLCO >= 80% of predicted
(2) FVC >= 80% of predicted
(3) absence of bibasilar rales
(4) no evidence of fibrosis on chest X-ray
(5) no evidence of pulmonary hypertension
Criteria for Grade 1 (mild) - all of the following:
(1) NOT Grade 0, 3 or 4
(2) DLCO >= 70% of predicted
(3) FVC >= 70% of predicted
Criteria for Grade 2 (moderate): NOT Grade 0, 1, 3 or 4
Criteria for Grade 3 (severe) - both of the following:
(1) one or more of the following (OR):
(1a) DLCO < 50%
(1b) FVC < 50%
(1c) moderate to severe pulmonary hypertension
(2) oxygen not required
Criteria for Grade 4 (endstage): oxygen required
