Secondary Budd-Chiari Syndrome Associated with Hepatic Echinococcosis

 

The Budd-Chiari syndrome may develop:

(1) with either cystic or alveolar echinococcosis.

(2) with compression of the hepatic veins and/or inferior vena cava (IVC)

 

The patient develops portal hypertension, hepatomegaly and ascites. Additional clinical findings may include:

(1) abdominal pain

(2) edema of the lower extremities

(3) gastrointestinal bleeding

(4) hepatic failure

 

Imaging studies demonstrate the parasitic cyst(s) and/or vascular compression.

 

Therapy may include:

(1) excision of the parasitic mass

(2) portosystemic shunt surgery

(3) liver transplant

(4) stent placement